Neonatal compartment syndrome is a rare condition mainly involving the upper extremity with ulcerated and necrotic lesions. It should be evaluated in detail due to the similarity with other conditions like necrotizing fasciitis, neonatal gangrene, and congenital varicella, etc. Early diagnosis and treatment have a paramount importance for the best outcome. To emphasize this, we would like to present a newborn with the forearm compartment syndrome diagnosed promptly and treated surgically.